Polygonal cells arranged in sheets and lobules; bound by thin fibrous septa
Abundant clear cytoplasm; occasional vacuolation
Peripherally located small monomorphic nuclei
Spindle-stellate cells present in areas of myxoid stroma
RNA-Seq: CLK1::PLAG1 gene fusion
Polygonal cells arranged in sheets and lobules; bound by thin fibrous septa
Abundant clear cytoplasm; variable vacuolation and size, based on extent of maturation
Peripherally located small monomorphic nuclei
Spindle-stellate cells present in areas of myxoid stroma
Often associated with PLAG1- or HMGA2-rearrangement; many potential partners (PMID: 32692992)