Pathology: papillary intralymphatic angioendothelioma

Papillary intralymphatic angioendothelioma (PILA)

  • Polypoid; ectatic vasculature lined by endothelial cells with prominent intraluminal fibrovascular papillae

  • Eosinophilic cytoplasm

  • Monomorphic round-ovoid nuclei with small nucleoli and "hobnailing"; inconspicuous mitotic activity

  • Occasional intraluminal proteinaceous material; mild-moderate chronic inflammatory infiltrate

  • IHC: D240