Pathology: myoepithelioma-like hyalinizing epithelioid tumour

Myoepithelioma-like hyalinizing epithelioid tumour

  • Lobulated

  • Loose fascicles of polygonal-spindle cells

  • Pale eosinophilic cytoplasm

  • Round-ovoid-reniform with minimal atypia and pin-point nucleoli; inconspicuous mitotic activity

  • Abundant hyalinized stroma

  • IHC: CD34

  • RNA-seq: OGT::FOXO4 gene fusion

  • PMID: 32649321, 31567281, 33455033